Prune belly syndrome (PBS) is a rare but morbid congenital disease, classically defined by a triad of cardinal features that includes cryptorchidism, urinary tract dilation and laxity of the abdominal wall musculature. Children often require numerous surgical inter- ventions including bilateral orchidopexy as well as individually tailored urinary tract and abdominal wall reconstruction. Along with the classic features, patients with PBS often experience gastrointestinal, orthopedic, and cardiopulmonary comorbidities. Keywords:
CITATION STYLE
Arlen, A. M., Nawaf, C., & Kirsch, A. J. (2019). Prune belly syndrome: current perspectives. Pediatric Health, Medicine and Therapeutics, Volume 10, 75–81. https://doi.org/10.2147/phmt.s188014
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