Isolated Right-Sided Endomyocardial Fibroelastosis Resulting in Sudden Cardiac Death

Abstract

Restrictive cardiomyopathy, atrial fibrillation, and cardiac thrombi have been reported with endomyocardial fibroelastosis. This case report examines a unique case of focal endomyocardial fibroelastosis localized to the right ventricle that resulted in sudden cardiac death in an otherwise healthy 21-year-old adult and discusses cardiac magnetic resonance imaging findings in this disease. (Level of Difficulty: Beginner.)