Nonsyndromic oligodontia - A rare case report

Abstract

Oligodontia is a rare congenital disorder which clinically presents as missing six or more teeth in deciduous, permanent, or both dentitions. Usually, oligodontia is seen as a part of few syndromes rarely occurs as an isolated entity. Msh homeobox 1 and paired box 9 genes are found to be responsible for nonsyndromic oligodontia. We present a case report a 17-year-old male patient, who had the absence ofmultiple teeth. General physical examination revealed there was no abnormality in either hair or nails, perspiration was normal and no congenital clefts of lip or palate were seen suggesting that he was not suffering from any syndromes. Hence, in our case, oligodontia was not associated with any syndrome which is a rare finding.