Cardiac abnormalities during anesthesia in a child with Prader Willi syndrome

Abstract

Concurrent hypotonia, hypomentia, hypogonadism, and obesity is a description of a particular congenital disturbance, first described in 1956, and referred to as the 'Prader Willi syndrome. By 1974, fewer than 200 cases had been reported. These cases demonstrate that despite a number of common characteristics, significant variability exists, particularly in growth deficiency and intellectual capability, suggesting that the heart arrhythmia found may be another expression of the Prader Willi syndrome.