Extensive intracranial juvenile xanthogranulomas

Abstract

JXG is a disorder classified under histiocytosis. It usually affects children and commonly presents with skin lesions. Intracranial lesions are uncommon and usually solitary. We present the case of a child who had extensive intracranial involvement with multiple enhancing solid lesions in the cerebellum, Brain stem, thalami, and bilateral cerebral hemispheres on MR imaging.