Consensus statement on the diagnosis and treatment of autoimmune nodopathies from the Peripheral Neuropathy Association of the Chinese Society of Neurology

Abstract

Autoimmune nodopathis are a group of immune-mediated peripheral neuropathy, with antibodies to Ranvier nodal regions that includes anti-NF155, contactin1 (CNTN1), and contactin-associatedprotein1 (Caspr1) antibodies. Clinical features, neurophysiology, cerebrospinal fluid test, peripheral nerve imaging, sural neuropathology and antibody detection, diagnostic criteria were summarized in this consensus, as well as suggested principles of treatment with rituximab, glucocorticoids, plasma exchange and other immunotherapy medicines.