Crossed fusion of renal pelves and Klippel Feil syndrome

Abstract

The high incidence of genitourinary anomalies in patients with the Klippel Feil syndrome (short neck, limitation of neck motion and low posterior hairline) has been defined by Moore et al. (1975). They found that 25 of 39 individuals (64%) with this syndrome had significant anomalies. Unilateral renal agenesis was the most common finding. IVP should be done on all patients with this condition. Still, congenital fusion of the renal pelves is a rare malformation and usually associated with fusion of the kidneys. The first case of surgically proved separate kidneys with crossed fusion of the renal pelves is reported. Operation was performed when the male patients was 18 yr old. He had a spina bifida and a meningomyelocele as well.