Pregnancy and the various forms of the Fontan circulation

Abstract

The Fontan operation is performed on those with highly complex congenital heart disease and has improved the survival and quality of life of such patients. Inevitably there are late complications secondary to extensive surgery and long-term survival estimates are about 70% at 10 years and 60-63% at 15 years. Pregnancy therefore requires careful prior consideration. However, the opinion that that pregnancy is not advisable for the Fontan patient is somewhat contentious and maybe an oversimplification of what is a highly emotive and complex issue.