Unanticipated difficult intubation in a child with Beals-Hecht syndrome presenting for emergency surgery

Abstract

Beals–Hecht syndrome is characterized by multiple joint contractures, arachnodactyly and kyphoscoliosis. We report the successful management of a patient diagnosed with Beals-Hecht syndrome who had micrognathia, a high arched palate and restricted mouth opening, who presented to us in the emergency for exploratory laparotomy. Oral intubation was successfully performed using aI-gel supraglottic airway as a conduit for intubation.