Idiopathic Hypertrophic Pachymeningitis

Abstract

Pachymeningitis is a rare inflammatory disease characterized by limited or widespread thickening of the dura mater. The clinical picture of this pathological condition is nonspecific and includes headache, damage to cranial nerves, blurred vision with papilledema, limb weakness, cerebellar symptoms, sensory impairment, and sensorineural hearing loss. An early administration of glucocorticosteroid therapy improves its course and prognosis.