Congenital icthyosiform--a case report.

Abstract

Congenital icthyosis is a rare group of disorders of keratinisation. A case of this condition is reported in order to highlight the clinical features and essential components of management: resuscitation, skincare, nutrition and counselling. This case is reported in order to appraise clinicians of its presence because there was delay in the diagnosis and management due to non-recognition.