Left ventricular noncompaction

Abstract

Left ventricular noncompaction (LVNC) is a cardiomyopathy associated with sporadic or familial disease, the latter having an autosomal dominant mode of transmission. Echocardiography is the current gold standard for diagnosis of this entity, but with the risk of over diagnosis and under diagnosis. There are frequent doubtful cases, that need multimodality confirmation (echocardiography and magnetic resonance imaging). The clinical features associated with LVNC vary from asymptomatic to symptomatic patients, with the potential for heart failure, supraventricular and ventricular arrhythmias, thrombo embolic events, and sudden cardiac death. There is no therapy specific for patients with LVNC. The treatment focuses on the complications of the disease.