A rare association of inflammatory myofibroblastic tumor of maxilla and idiopathic orbital inflammatory disease

Abstract

Inflammatory myofibroblastic tumor (pseudotumor) is a rare tumor belonging to the family of fibrous mesenchymal tumors. Though it usually involves lungs, but extrapulmonary site involvement, especially head and neck region is rare. In this paper, we are presenting a 26-year-old male patient, with inflammatory myofibroblastic tumor of maxilla, with a rare association with a prior history of idiopathic orbital inflammatory disease, treated medically. The patient was treated surgically with complete excision of the pathology from maxilla. This case report intents to review the controversies in management of this tumor and also to enlighten the possible association between the orbital and maxillary pseudotumor.