Hirschsprung’s Disease in Adult Treated by Coloprotectomy and Colo-Anal Anastomosis

Abstract

Hirschsprung’s disease is a rare pathology Most cases become manifest during the neonatal period, but in rare instances, the disease is initially diagnosed in adult patients. We report a case of the 26 years old man who presented a Hirschsprung disease. Developed severe intestinal obstruction and presented to the emergency department with significant abdominal distension. A computed tomographic scan confirmed significant fecal loading of the entire colon and rectum. The diagnosis was established through peroperatively biopsy. A rectal biopsy showing aganglionic anorectum. The treatment consist in a coloproctectomy with coloanal anastomosis. The postoperative course was uneventful with complete resolution of the symptoms. Hirschsprung’s disease should be considered in adults who have long-standing and refractory constipation.