Rare primary central nervous system tumors

Abstract

An estimated 69,720 new cases of primary central nervous system tumors are expected to be diagnosed in 2013 based on projection using the 2013 Central Brain Tumor Registry of the United States (CBTRUS) Statistical Report (www.cbtrus.org). Meningiomas, gliomas, nerve sheath tumors, and pituitary tumors together constitute more than 85% of all primary central nervous system tumors diagnosed in the US. There are some tumors which constitute less than 1% of all brain tumors. The purpose of this paper is to provide an overview of the clinical, pathologic and therapeutic aspects of some of the more commonly encountered rare primary brain tumors, including atypical teratoid/rhabdoid tumor, choroid plexus carcinoma, ganglioglioma, hemangiopericytoma, and pleomorphic xanthoastrocytoma. & copy; C.D. Kubicky et al., 2014.