A 21‐Year‐Old Man with Systemic‐Onset Juvenile Rheumatoid Arthritis, Cough and Progressive Dyspnea

Abstract

Primary or nonobstructive, endogenous lipoid pneumonia is a rare clinical entity usually associated with an underlying systemic disease. The present report describes a case involving a 21‐year‐old man with systemic‐onset juvenile rheumatoid arthritis who developed primary endogenous lipoid pneumonia. Multiple treatment regimens were attempted; however, definitive management was only achieved through double‐lung transplantation.