Hipertensão arterial pulmonar

Abstract

Pulmonary arterial hypertension (PAH) is a progressive and severe disease which is associated with increased morbidity and mortality. In the past decade, new specific drugs were developed for its treatment: these advances led to improved disease control and better prognosis. It should be noted, however, that the diagnosis of PAH is of exclusion and several evaluation steps should be followed before a definitive diagnosis can be made. Although there are several algorithms for diagnosis and treatment of the disease, an individual approach should always be pursued. The present review summarizes the most relevant advances on diagnosis and treatment of PAH, with special emphasis in the prognostic evaluation. © Copyright Moreira Jr. Editora.