Low-grade fibromyxoid sarcoma as a content of perineal hernia. A case report

Abstract

Background: Low-grade fibromyxoid sarcoma is a rare neoplasm with apparently benign histology but with late aggressive metastatic behavior. The perineal hernias are unusual, there are no more than 100 cases reported in the world literature. Discussion: The presentation of this fibroblastic neoplasm is rare and makes it even more rare if it is as the content of a primary perineal hernia. Conclusion: It is an infrequent neoplasm that occurs in approximately 0.7% of all cases, with aggressive metastatic behavior and in need of adjuvant treatment.