Möebius Syndrome, What Anesthesiologist Should Consider About: A Case Report

Abstract

First described in 1888, Möebius syndrome is a variety of cranial nerve palsy combinations mainly involving sixth, seventh and eighth cranial nerves. Although rare, affected infants and children might be referred to anesthesiologists for many types of ophthalmologic or otologic surgeries. Data on anesthetic management of such patients are scarce and case reports can be a source of useful information for anesthesiologists throughout the world. Since it involves facial muscles and their development, affected patient potentially may be a case of difficult airway as well; although it is rare. Malignant hyperthermia is another potential threat. We report a known case of Möebius syndrome candidate for cochlear implantation under general anesthesia. Although our case was uneventful, the anesthesiology team has to be prepared for potential risks such as difficult airway management or malignant hyperthermia in these patients.